Pulmonary hypertension: a fatal complication of neurofibromatosis type 1.
نویسندگان
چکیده
We report a very rare case of severe pulmonary arterial hypertension in a patient with neurofibromatosis type 1, and discuss the pathology, pathogenesis, current pulmonary hypertension classification system, and outcomes of pulmonary arterial hypertension in patients with neurofibromatosis type 1.
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ورودعنوان ژورنال:
- Respiratory care
دوره 56 11 شماره
صفحات -
تاریخ انتشار 2011